Congenital heart disease with its worldwide incidence of 1% is the most common inborn defect. Increasingly, patients are living into adulthood, with ongoing congenital heart and other medical needs. Sadly, only a small minority have specialist follow-up. However, all patients see their family doctor and may also seek advice from other health professionals. This practical guide with its straightforward a,b,c approach is written for those professionals. Special features of this book: Introduces the principles of congenital heart disease and tells you whom and when to refer for specialist care Discusses common congenital heart lesions in a practical, easy-to-follow way, with an emphasis on diagnosis and management issues Includes an extensive chapter on 'Pregnancy and Contraception' (by Philip J. Steer), essential both for family planning and for managing safely the pregnant woman with congenital heart disease Includes chapters on non-cardiac surgery and lifestyle issues such as work, insurability, travel and driving Provides invaluable information on dealing with common emergencies; what to do and what not to do With a wealth of illustrations (including diagrams, EKGs, CXRs, Echos and cardiac MRIs) and with key point tables, this is an essential guide for all health care professionals managing patients with adult congenital heart disease.

Congenital heart disease with its worldwide incidence of 1% is themost common inborn defect. Increasingly, patients are living intoadulthood, with ongoing congenital heart and other medical needs.Sadly, only a small minority have specialist follow-up. Howeverall patients see their family doctor and may also seek advice fromother health professionals.This practical guide with its straightforward a,b,c approach iswritten for those professionals.Special features of this book:* Introduces the principles of congenital heart diseaseand tells you whom and when to refer for specialist care* Discusses common congenital heart lesions in a practicaleasy-to-follow way, with an emphasis on diagnosis and managementissues* Includes an extensive chapter on 'Pregnancy andContraception' (by Philip J. Steer), essential both for familyplanning and for managing safely the pregnant woman with congenitalheart disease* Includes chapters on non-cardiac surgery and lifestyleissues such as work, insurability, travel and driving* Provides invaluable information on dealing with commonemergencies; what to do and what not to doWith a wealth of illustrations (including diagrams, EKGs, CXRsEchos and cardiac MRIs) and with key point tables, this is anessential guide for all health care professionals managing patientswith adult congenital heart disease.

Foreword viiPreface ixAcknowledgments xPart 1 General Principles 11 Epidemiology of Congenital Heart Disease 32 Services for the Adult with Congenital Heart Disease 83 Pregnancy and Contraception 164 Infective Endocarditis Prophylaxis 365 Anticoagulation 426 Lifestyle Issues 497 Long-Term Outcome 60Part 2 Common Lesions 658 Atrial Septal Defects and Anomalous Pulmonary Venous Drainage 679 Ventricular Septal Defect 8210 Atrioventricular Septal Defect 8711 Left Ventricular Outfl ow Tract Disorders 9212 Coarctation of the Aorta 9713 Complete Transposition of the Great Arteries 10314 The Single Ventricle and Fontan Circulations 11215 Tetralogy of Fallot and Right Ventricular Outfl ow Tract Disorders 12516 Pulmonary Atresia with Ventricular Septal Defect 13217 Ebstein's Anomaly of the Tricuspid Valve 13918 Patent Arterial Duct 14519 Marfan Syndrome 15320 Eisenmenger Syndrome 16121 Other Lesions 17422 Pulmonary Hypertension 182Part 3 Emergencies and Special Situations 18923 Arrhythmia and Syncope 19124 Suspected Infective Endocarditis 19625 Perioperative Care 20126 Heart Failure: Acute Management 20627 Care of the Cyanosed Patient 209Bibliography 213Glossary 217Appendix: Shunt Calculations 257Index 261